Idiopathic pulmonary fibrosis

Also known as: ILD · interstitial lung disease · IPF

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United StatesATS/CHEST

Current

Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline

ATS / ERS / JRS / ALAT · 2022

A four-society international guideline that updates earlier IPF recommendations and, for the first time, defines progressive pulmonary fibrosis in interstitial lung diseases other than IPF.

Radiological and histopathological criteria for diagnosing IPF were revised by expert consensus. source
Systematic reviews and GRADE were used to address transbronchial lung cryobiopsy, genomic classifier testing, antacid medication and antireflux surgery. source

Verify against original ↗

EuropeERS (global: GOLD/GINA)

No ERS (global: GOLD/GINA) guideline indexed for this condition yet.

Every entry is added by hand and cited to the issuing society, so a gap here means we have not verified one — not that none exists. Know the right one? Tell us.

US vs EU key differences

No curated US/EU comparison yet for this disease.

What changed recently

US2018 → 20222022-05-01
The 2022 update revises the radiological and histopathological criteria for IPF by consensus and adds evidence-based recommendations on transbronchial lung cryobiopsy, genomic classifier testing, antacid medication and antireflux surgery. It also extends beyond IPF for the first time by defining and giving guidance on progressive pulmonary fibrosis in other interstitial lung diseases.
source ↗curation confidence 90%

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